Surgical Outcome of Hirschsprung’s Disease in Male Child: A Rare Case Report

Abstract

Introduction: This disorder characterized by absence of particular nerve cells (ganglions) in a segment of the bowel in an infant. Ganglion cell absence allows the muscles of the intestines to lose their capacity to pass faeces across the peristalsis of the intestine. This condition affects the large intestine and causes problem with passing stool. The condition is congenital. In around 1 out of 5000 live births, Hirschsprung disease occurs and is three times more frequent in boys than girls. About 12% of cases are due to genetic disorders. Patient history: A 2 years old male was admitted in A.V.B.R. Hospital in paediatric ward. His chief complaint was inability to pass stools on his own, fever, vomiting, constipation. Paediatric history: This male child was born by Lower segment caesarean section. At the age of 17 months, the complaint started with inability to pass stool on his own. After that his parents approached A.V.B.R. Hospital and Doctor advised for further medical and surgical management. Main symptoms and importance of clinical findings: The patient had undergone various investigations like blood tests, USG, Physical examination and. rectal biopsy and per abdominal x-ray. Medical Management: Patient was treated with trans-anal endorectal pull through surgery under general anaesthesia Nursing management: Administered fluid replacement i.e. DNS and RL, monitored all vital signs checked 8 hourly. Conclusion: The 2 years old male was admitted in A.V.B.R. Hospital in paediatric ward. His chief complaint was inability to pass stools on his own, fever, vomiting, constipation etc. after undergoing investigation he was diagnosed as Hirschsprung’s disease.