Cervicothoracic Lymphangioma in an Adult: A Rare Entity

Abstract

Background: Lymphangiomas are uncommon benign lymphatic malformations most commonly seen in the head and neck region. Cervical lymphangiomas with intrathoracic extension are very rare clinical entity and comprise only 1% of the cases. Case Report: We report here a rare case of a 25 year old female, with complaints of a huge soft, cystic fluctuant and transilluminant swelling involving the right side of the neck and chest. On imaging, it revealed a multilocular thoracocervical mass, which was isointense on T1 and hyperintense on T2, occupying right anterosuperior, middle and posterior mediastinum compressing the upper lobe of the right lung and extending supraclavicularly. Patient was managed surgically via multidisciplinary approach. Histopathological examination confirmed the diagnosis of lymphangioma Discussion and Conclusion: Imaging and histopathological examination play a key role in diagnosis of lymphangiomas. Such extensive lymphangiomas require complete surgical excision and should be performed by experienced surgeons as this is essential to prevent further recurrences.