Unicuspid Aortic Valve: An Adult Case Report

Abstract

The unicuspid aortic valve is a very rare congenital disease that usually presents in the 3rd to 5th decade of life-and usually with severe aortic stenosis or regurgitation. Diagnosis can be made with 2- or 3-dimensional transthoracic or transesophageal echocardiography. It is mostly complicated by aortic dilatation and left ventricular hypertrophy. We present the case of a 35 years old, symptomatic patient with a unicuspid aortic valve, complicated by dilatation of the ascending aorta, with left ventricular hypertrophy.