A Rare Case of Nasal Polyposis in Hurler Syndrome

Abstract

Mucopolysaccharidosis (MPS) type I is a rare multisystem disorder resulting from the accumulation of breakdown products of glycosaminoglycans in the body tissues. Many patients with this disease undergo ENT surgeries as adenotonsillectomy. Nasal polyposis is a rare occurrence. The aim of this work is to present a very rare association observed in an 8-years-old patient with Hurler syndrome treated in the ENT Head and Neck Surgery department of Ibn Rochd University Hospital Casablanca, for nasal polyposis and adenoid hypertrophy.