Hemoptysis in a Young Adult with Congenital Cystic Adenomatoid Malformation of the Lung: Case Report

Abstract

Congenital cystic adenomatoid malformations (CCAM), also named congenital pulmonary airway malformation s (CPAM) are multicystic masses of segmental lung tissue with abnormal bronchial proliferation. There is failure of normal bronchoalveolar development with a hamartomatous proliferation of terminal respiratory units in a gland-like pattern (adenomatoid). CPAM can be divided into five types, according to clinical and pathologic features. [1] CPAM type 1 is the most common, and has good prognosis. The widespread use of antenatal ultrasound examination has resulted in an increase in the prenatal diagnosis of CPAM [2]. The diagnosis may not be made for many years or even until adulthood when the abnormality is small. With recurrent chest infection it does become apparent [3,4]. This case report documents young male patient with hemoptysis, and right lower lobe t variable sized cysts for which he underwent right thoracotomy with right lower lobectomy. The histopathology tissue report showed feature of congenital pulmonary airway malformation, Type 1(CPAM1).