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Research Article Open access CC BY 4.0

Familial Idiopathic Basal Ganglia Calcification (Fahr's syndrome): Initial Clinical Neuropsychiatric Presentation without Corresponding Neurological Deficit

Malte Christian Claussen, Katayun Hassanpour, Josef Jenewein, Soenke Boettger

International Neuropsychiatric Disease Journal · pp. 1–5 · Published 20 Jun 2017

10.9734/INDJ/2017/34524

Abstract

Familial idiopathic basal ganglia calcification (FIBGC) or Fahr's syndrome is a rare disorder with various clinical presentations which can mimic - in particular - psychiatric illness. The following case is characterized by the typical basal ganglia calcifications and presentation of neuropsychiatric symptoms indicating the first clinical presentation in the absence of a neurological deficit. As previously reported, the extent of calcification did not predict neurological impairment, however, predicted severe psychosis.

Basal ganglia calcification familial idiopathic basal ganglia calcification (FIBGC) Fahr's syndrome neurological deficits psychosis extra-pyramidal symptoms

References (9)

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